ENTRY ko00250 Pathway NAME Alanine, aspartate and glutamate metabolism CLASS Metabolism; Amino acid metabolism PATHWAY_MAP ko00250 Alanine, aspartate and glutamate metabolism MODULE M00027 GABA (gamma-Aminobutyrate) shunt [PATH:ko00250] M00740 Methylaspartate cycle [PATH:ko00250] DBLINKS GO: 0006522 0006531 0006536 ORTHOLOGY K00135 gabD; succinate-semialdehyde dehydrogenase / glutarate-semialdehyde dehydrogenase [EC:1.2.1.16 1.2.1.79 1.2.1.20] K00139 ALDH5A1; succinate-semialdehyde dehydrogenase [EC:1.2.1.24] K00259 ald; alanine dehydrogenase [EC:1.4.1.1] K00260 gudB, rocG; glutamate dehydrogenase [EC:1.4.1.2] K00261 GLUD1_2, gdhA; glutamate dehydrogenase (NAD(P)+) [EC:1.4.1.3] K00262 E1.4.1.4, gdhA; glutamate dehydrogenase (NADP+) [EC:1.4.1.4] K00264 GLT1; glutamate synthase (NADH) [EC:1.4.1.14] K00265 gltB; glutamate synthase (NADPH) large chain [EC:1.4.1.13] K00266 gltD; glutamate synthase (NADPH) small chain [EC:1.4.1.13] K00272 DDO; D-aspartate oxidase [EC:1.4.3.1] K00278 nadB; L-aspartate oxidase [EC:1.4.3.16] K00294 E1.2.1.88; 1-pyrroline-5-carboxylate dehydrogenase [EC:1.2.1.88] K00608 pyrBI; aspartate carbamoyltransferase [EC:2.1.3.2] K00609 pyrB, PYR2; aspartate carbamoyltransferase catalytic subunit [EC:2.1.3.2] K00610 pyrI; aspartate carbamoyltransferase regulatory subunit K00764 purF, PPAT; amidophosphoribosyltransferase [EC:2.4.2.14] K00811 ASP5; aspartate aminotransferase, chloroplastic [EC:2.6.1.1] K00812 aspB; aspartate aminotransferase [EC:2.6.1.1] K00813 aspC; aspartate aminotransferase [EC:2.6.1.1] K00814 GPT, ALT; alanine transaminase [EC:2.6.1.2] K00820 glmS, GFPT; glutamine---fructose-6-phosphate transaminase (isomerizing) [EC:2.6.1.16] K00823 puuE; 4-aminobutyrate aminotransferase [EC:2.6.1.19] K00827 AGXT2; alanine-glyoxylate transaminase / (R)-3-amino-2-methylpropionate-pyruvate transaminase [EC:2.6.1.44 2.6.1.40] K00830 AGXT; alanine-glyoxylate transaminase / serine-glyoxylate transaminase / serine-pyruvate transaminase [EC:2.6.1.44 2.6.1.45 2.6.1.51] K01424 E3.5.1.1, ansA, ansB; L-asparaginase [EC:3.5.1.1] K01425 glsA, GLS; glutaminase [EC:3.5.1.2] K01437 ASPA; aspartoacylase [EC:3.5.1.15] K01580 E4.1.1.15, gadB, gadA, GAD; glutamate decarboxylase [EC:4.1.1.15] K01744 aspA; aspartate ammonia-lyase [EC:4.3.1.1] K01755 argH, ASL; argininosuccinate lyase [EC:4.3.2.1] K01756 purB, ADSL; adenylosuccinate lyase [EC:4.3.2.2] K01779 racD; aspartate racemase [EC:5.1.1.13] K01914 asnA; aspartate--ammonia ligase [EC:6.3.1.1] K01915 glnA, GLUL; glutamine synthetase [EC:6.3.1.2] K01939 purA, ADSS; adenylosuccinate synthase [EC:6.3.4.4] K01940 argG, ASS1; argininosuccinate synthase [EC:6.3.4.5] K01948 CPS1; carbamoyl-phosphate synthase (ammonia) [EC:6.3.4.16] K01953 asnB, ASNS; asparagine synthase (glutamine-hydrolysing) [EC:6.3.5.4] K01954 K01954; carbamoyl-phosphate synthase [EC:6.3.5.5] K01955 carB, CPA2; carbamoyl-phosphate synthase large subunit [EC:6.3.5.5] K01956 carA, CPA1; carbamoyl-phosphate synthase small subunit [EC:6.3.5.5] K03334 IL4I1; L-amino-acid oxidase [EC:1.4.3.2] K05597 aspQ, ansB, ansA; glutamin-(asparagin-)ase [EC:3.5.1.38] K07250 gabT; 4-aminobutyrate aminotransferase / (S)-3-amino-2-methylpropionate transaminase / 5-aminovalerate transaminase [EC:2.6.1.19 2.6.1.22 2.6.1.48] K08324 sad; succinate-semialdehyde dehydrogenase [EC:1.2.1.16 1.2.1.24] K08590 nit; 2-oxoglutaramate amidase [EC:3.5.1.111] K09758 asdA; aspartate 4-decarboxylase [EC:4.1.1.12] K11358 yhdR; aspartate aminotransferase [EC:2.6.1.1] K11540 CAD; carbamoyl-phosphate synthase / aspartate carbamoyltransferase / dihydroorotase [EC:6.3.5.5 2.1.3.2 3.5.2.3] K11541 URA2; carbamoyl-phosphate synthase / aspartate carbamoyltransferase [EC:6.3.5.5 2.1.3.2] K13051 ASRGL1, iaaA; L-asparaginase / beta-aspartyl-peptidase [EC:3.5.1.1 3.4.19.5] K13524 ABAT; 4-aminobutyrate aminotransferase / (S)-3-amino-2-methylpropionate transaminase [EC:2.6.1.19 2.6.1.22] K13566 NIT2, yafV; omega-amidase [EC:3.5.1.3] K13821 putA; RHH-type transcriptional regulator, proline utilization regulon repressor / proline dehydrogenase / delta 1-pyrroline-5-carboxylate dehydrogenase [EC:1.5.5.2 1.2.1.88] K14260 alaA; alanine-synthesizing transaminase [EC:2.6.1.66 2.6.1.2] K14268 davT, gabT; 5-aminovalerate/4-aminobutyrate aminotransferase [EC:2.6.1.48 2.6.1.19] K14272 GGAT; glutamate--glyoxylate aminotransferase [EC:2.6.1.4 2.6.1.2 2.6.1.44] K14454 GOT1, AAT2; aspartate aminotransferase, cytoplasmic [EC:2.6.1.1] K14455 GOT2; aspartate aminotransferase, mitochondrial [EC:2.6.1.1] K14592 FOLH1, GCPII; glutamate carboxypeptidase II (folate hydrolase 1) [EC:3.4.17.21] K14681 argHA; argininosuccinate lyase / amino-acid N-acetyltransferase [EC:4.3.2.1 2.3.1.1] K15371 GDH2; glutamate dehydrogenase [EC:1.4.1.2] K16871 POP2; 4-aminobutyrate---pyruvate transaminase [EC:2.6.1.96] K17761 SSADH; succinate-semialdehyde dehydrogenase, mitochondrial [EC:1.2.1.24] K18309 NAT8L; aspartate N-acetyltransferase [EC:2.3.1.17] K18310 RIMKLB, NAAGS-I; beta-citrylglutamate/N-acetylaspartylglutamate synthase [EC:6.3.1.17 6.3.2.41] K18311 RIMKLA, NAAGS-II; N-acetylaspartylglutamate/N-acetylaspartylglutamylglutamate synthase [EC:6.3.2.41 6.3.2.42] K19244 ala; alanine dehydrogenase [EC:1.4.1.1] K22457 E2.6.1.14; asparagine---oxo-acid transaminase [EC:2.6.1.14] K23265 purQ; phosphoribosylformylglycinamidine synthase subunit PurQ / glutaminase COMPOUND C00014 Ammonia C00022 Pyruvate C00025 L-Glutamate C00026 2-Oxoglutarate C00036 Oxaloacetate C00041 L-Alanine C00042 Succinate C00049 L-Aspartate C00064 L-Glutamine C00122 Fumarate C00152 L-Asparagine C00158 Citrate C00169 Carbamoyl phosphate C00232 Succinate semialdehyde C00334 4-Aminobutanoate C00352 D-Glucosamine 6-phosphate C00402 D-Aspartate C00438 N-Carbamoyl-L-aspartate C00940 2-Oxoglutaramate C01042 N-Acetyl-L-aspartate C02362 2-Oxosuccinamate C03090 5-Phosphoribosylamine C03406 N-(L-Arginino)succinate C03794 N6-(1,2-Dicarboxyethyl)-AMP C03912 (S)-1-Pyrroline-5-carboxylate C12270 N-Acetylaspartylglutamate C20775 beta-Citryl-L-glutamate C20776 N-Acetylaspartylglutamylglutamate REFERENCE AUTHORS Nishizuka Y, Seyama Y, Ikai A, Ishimura Y, Kawaguchi A (eds). TITLE [Cellular Functions and Metabolic Maps] (In Japanese) JOURNAL Tokyo Kagaku Dojin (1997) REFERENCE PMID:9687539 AUTHORS Wu G TITLE Intestinal mucosal amino acid catabolism. JOURNAL J Nutr 128:1249-52 (1998) DOI:10.1093/jn/128.8.1249 REL_PATHWAY ko00010 Glycolysis / Gluconeogenesis ko00020 Citrate cycle (TCA cycle) ko00220 Arginine biosynthesis ko00230 Purine metabolism ko00240 Pyrimidine metabolism ko00260 Glycine, serine and threonine metabolism ko00261 Monobactam biosynthesis ko00300 Lysine biosynthesis ko00330 Arginine and proline metabolism ko00340 Histidine metabolism ko00410 beta-Alanine metabolism ko00460 Cyanoamino acid metabolism ko00470 D-Amino acid metabolism ko00480 Glutathione metabolism ko00520 Amino sugar and nucleotide sugar metabolism ko00620 Pyruvate metabolism ko00630 Glyoxylate and dicarboxylate metabolism ko00650 Butanoate metabolism ko00660 C5-Branched dibasic acid metabolism ko00760 Nicotinate and nicotinamide metabolism ko00770 Pantothenate and CoA biosynthesis ko00860 Porphyrin metabolism ko00910 Nitrogen metabolism ///